• Medientyp: E-Artikel
  • Titel: Aplasia Cutis Congenita Associated with Fetus Papyraceus
  • Beteiligte: Pieretti, María Lía; Alcalá, Rebeca; Boggio, Paula; Noguera‐Morel, Lucero; Porriño, María Librada; Luna, Paula C.; Hernández‐Martín, Angela; Schroh, Roberto; Larralde, Margarita; Torrelo, Antonio
  • Erschienen: Wiley, 2015
  • Erschienen in: Pediatric Dermatology
  • Sprache: Englisch
  • DOI: 10.1111/pde.12651
  • ISSN: 0736-8046; 1525-1470
  • Schlagwörter: Dermatology ; Pediatrics, Perinatology and Child Health
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  • Beschreibung: <jats:title>Abstract</jats:title><jats:p>Aplasia cutis congenita (<jats:styled-content style="fixed-case">ACC</jats:styled-content>), or congenital absence of skin, is a heterogeneous condition that may be due to varied mechanisms. <jats:styled-content style="fixed-case">ACC</jats:styled-content> has rarely been reported in association with fetus papyraceus, representing a peculiar phenotype of <jats:styled-content style="fixed-case">ACC</jats:styled-content>. We present six new cases of neonates born with symmetric <jats:styled-content style="fixed-case">ACC</jats:styled-content> associated with intrauterine fetal demise of co‐twins during the late first or early second trimester.</jats:p>