Beschreibung:
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<jats:title>Background: </jats:title>
<jats:p>Gorham-Stout disease (GSD) is a rare syndrome presenting with progressive osteolysis which in the spine can lead to cord injury, instability, and deformity. Here, the early spine surgery may prevent catastrophic outcomes.</jats:p>
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<jats:title>Case Description: </jats:title>
<jats:p>A 25-year-old male with GSD involving the T2 to T6 levels presented with acute traumatic kyphoscoliosis at T3 and T4 and left lower extremity paraparesis. The CT scan 4 weeks before this showed progressing osteolysis versus the CT 5 years ago. Unfortunately, the patient underwent delayed treatment resulting in permanent neurological sequelae. Surgery included a laminectomy and vertebrectomy of T3/T4 with instrumented fusion from T1-10. The use of the spinal instability neoplastic score (SINS) is a useful tool to prompt early referral to spine surgeons.</jats:p>
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<jats:title>Conclusion: </jats:title>
<jats:p>We recommend using the SINS score in GSD patients who develop spinal lesions to prompt early referral for consideration of surgery.</jats:p>
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